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Brain–blood amino acid correlates following protein restriction in murine maple syrup urine disease
Journal article   Open access  Peer reviewed

Brain–blood amino acid correlates following protein restriction in murine maple syrup urine disease

Kara R Vogel, Erland Arning, Brandi L Wasek, Sterling McPherson, Teodoro Bottiglieri and K Michael Gibson
Orphanet journal of rare diseases, Vol.9(1), pp.73-73
05/08/2014
Handle:
https://hdl.handle.net/2376/102799
PMCID: PMC4022424
PMID: 24886632
url
https://doi.org/10.1186/1750-1172-9-73View
Published (Version of record) Open

Abstract

Large neutral aminoacidopathies Branched-chain keto-acid dehydrogenase (BCKDH) complex Maple syrup urine disease (MSUD) Branched-chain amino acids (BCAAs) Mouse model Research Large neutral amino acid transporter (LAT-1) Phenylketonuria (PKU) Dietary protein restriction

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